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XLeu Maxamum®

A leucine-free powdered medical food for the dietary management of isovaleric acidemia and other proven disorders of leucine metabolism in children over 8 years and adults, including maternal patients.

Price: $667.39

 

Features

  • Leucine-free
  • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements (including iron, selenium and chromium)
  • Age-appropriate DRI formulation
  • XLeu Maxamum provides 40 g of protein equivalent per 100 g of powder
  • Available in orange flavor
  • Does not contain fat thereby allowing greater flexibility in modifying energy intake

Indications

  • Isovaleric acidemia
  • Other proven disorders of leucine metabolism

Nutrition

Nutrients Per 100g Per 10g Protein
Equivalent
Calories 305 76
Protein Equivalent,g 40 10
Fat, g <1 <0.25
Carbohydrate, g 34 8.5
 
Amino Acids,g Per 100g Per 10g Protein
Equivalent
L-Alanine 2.2 0.55
L-Arginine 3.6 0.9
L-Aspartic Acid 3 0.75
L-Cystine 1.3 0.33
L-Glutamic Acid 3.9 0.98
Glycine 6.3 1.58
L-Histidine 2.1 0.53
L-Isoleucine 1.2 0.3
L-Leucine None None
L-Lysine 3 0.75
L-Methionine 0.86 0.22
L-Phenylalanine 2.3 0.58
L-Proline 6.3 1.58
L-Serine 1.9 0.48
L-Threonine 2.1 0.53
L-Tryptophan 0.79 0.2
L-Tyrosine 2.3 0.58
L-Valine 1.4 0.35
L-Carnitine 0.039 0.01
Taurine 0.14 0.04
L-Glutamine 0.32 0.08
 
Vitamins Per 100g Per 10g Protein
Equivalent
Vitamin A, IU (mcg R.E.) 2228(669) 557 (167)
Vitamin D, IU (mcg) 332(8.3) 83 (2.1)
Vitamin E, IU (mg a T.E.) 18.3(12.3) 4.6 (3.1)
Vitamin K, mcg 82 21
Thiamine, mg 0.91 0.23
Riboflavin, mg 0.97 0.24
Vitamin B6, mg 1.6 0.4
Vitamin B12, mcg 3.1 0.8
Niacin, mg 5.7 1.4
Folic Acid, mcg 491 123
Pantothenic Acid, mg 4.9 1.2
Biotin, mcg 24.5 6.1
Vitamin C, mg 62 16
Choline, mg 430 108
Inositol, mg 80 20
 
Minerals Per 100g Per 10g Protein
Equivalent
Calcium, mg 1183 296
Phosphorus, mg 1137 284
Magnesium, mg 306 77
Iron, mg 14.7 3.7
Zinc, mg 9 2
Manganese, mg 1.8 0.5
Copper, mcg 820 205
Iodine, mcg 131 33
Molybdenum, mcg 37 9
Chromium, mcg 26 7
Selenium, mcg 58 15
Sodium, mg(mEq) 560(24.3) 140 (6.1)
Potassium, mg(mEq) 700(17.9) 175 (4.5)
Chloride, mg(mEq) 560(16) 140 (4)

Ingredients

Sugar, L-Lysine L-Glutamate, L-Proline, Glycine, Corn Syrup Solids, Calcium Phosphate Dibasic, L-Arginine, L-Aspartic Acid, L-Phenylalanine, Artificial Flavor, L-Tyrosine, L-Alanine, L-Threonine, Citric Acid, L-Histidine , L-Serine, Magnesium Acetate, L-Valine, L-Cystine, L-Isoleucine, Tripotassium Citrate, Choline Bitartrate, Sodium Chloride, L-Methionine, L-Glutamic Acid, L-Tryptophan, Soy Lecithin, Disodium Hydrogen Phosphate, Dipotassium Hydrogen Phosphate, L-Glutamine, Tricalcium Phosphate, Taurine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, L-Carnitine, Zinc Sulfate, DL-Alpha Tocopheryl Acetate, Niacinamide, Manganese Sulfate, Calcium Dpantothenate, Cupric Sulfate, Pyridoxine Hydrochloride, Sodium Selenite, Thiamine Chloride Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Artificial Colors (Beta-Carotene, Beet Red), Potassium Iodide, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin.

Preparation & Storage

Directions for Preparation and Use
Maxamum must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet protein and general nutrient requirements.

The recommended intake of Maxamum will vary depending on the age, bodyweight and medical condition of the individual. Intake should be adjusted to maintain normal growth and development. For accuracy, Maxamum should be weighed on a gram scale. The daily intake of Maxamum should be divided into equal portions and distributed throughout the day.

Maxamum is best served with meals. Make a paste of the prescribed amount of powder with a small volume of chilled water. Gradually add sufficient water to make the desired volume. It is recommended that Maxamum be prepared at a 1 to 7 dilution (e.g. 35 g (approx 1/4 cup) of powder plus 245 mL (approx. 8 fl oz) of water) and advanced to a 1 to 5 dilution (e.g. 35 g (approx 1/4 cup) of powder plus 175 mL (approx. 6 fl oz) of water). These dilutions are guidelines only. Maxamum may be given in a more concentrated form (e.g. drink or paste). If so, water or diluted drinks should be offered at the same time. For best taste, consume immediately. Larger volumes of prepared drink mix should be refrigerated and used within 24 hours or preparation.
Maxamum Range
(Flavored & Unflavored)

Measure Weight

1 Cup

145 g

1/2 Cup

 70 g

1/4 Cup

35 g

1 Tbsp

9 g

Precaution
Must only be consumed by individuals with proven isovaleric acidemia while under strict medical supervision. Not intended for children under nine years of age. Not suitable as a sole source of nutrition. Not for parenteral use.

Storage

Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

Ordering Information


Product Code
Reimbursement Code
HCPCS Code
Product Packaging
Calories Per Unit

117790 49735-0177-90 B4157 or B4162 6 x 454 g (1 lb) 1385
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