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Features
- Lysine-free
- Low in tryptophan to prevent deficiency
- Contains arginine
- Complete with vitamins and minerals developed specifically to help meet needs of children with GA-1
- Provides 25 g of protein equivalent per 100 g of powder
- Supplemented with flaxseed oil to provide a good source of Omega-3 fatty acids
- Osmolalilty (mOsm/kg): 797 Based on a standard dilution of 40 g powder to 7 fl oz water (210 mL)
Indication
Glutaric acidemia type I
Nutrition
| Nutrients |
Per 100 g Powder
|
Per 10 g Protein
Equivalent (1 Scoop) |
| Calories |
385
|
154
|
| Protein Equivalent, g |
25
|
10
|
| Amino Acids, g |
30
|
12
|
| Lysine, mg |
0
|
0
|
| Arginine, mg |
2704
|
1082
|
| Tryptophan, mg |
150
|
60
|
| Carbohydrate, g |
45
|
18
|
| Soluble Fiber, g |
3.9
|
1.5
|
| Fat, g |
13
|
5
|
| Saturated Fat, g |
2.3
|
0.92
|
| Monounsaturated Fat, g |
7.6
|
3
|
| Polyunsaturated Fat, g |
2.9
|
1.1
|
| Linoleic Acid, mg |
2232
|
893
|
| a-Linolenic Acid, mg |
687
|
275
|
| Amino Acids, g |
Per 100 g Powder
|
Per 10 g Protein
Equivalent (1 Scoop) |
| L-Alanine | 1.2 | 0.48 |
| L-Arginine | 2.7 | 1.08 |
| L-Asparagine | 1.8 | 0.72 |
| L-Cystine | 0.45 | 0.18 |
| L-Glutamic Acid | 0.9 | 0.36 |
| L-Glutamine | 4.51 | 1.8 |
| Glycine | 0.6 | 0.24 |
| L-Histidine | 0.9 | 0.36 |
| L-Isoleucine | 2.1 | 0.84 |
| L-Leucine | 3.46 | 1.38 |
| L-Lysine | 0 | 0 |
| L-Methionine | 1.02 | 0.41 |
| L-Ornithine | 0.6 | 0.24 |
| L-Phenylalanine | 1.59 | 0.64 |
| L-Proline | 1.5 | 0.6 |
| L-Serine | 0.6 | 0.24 |
| L-Threonine | 1.59 | 0.64 |
| L-Tryptophan | 0.15 | 0.06 |
| L-Tyrosine | 1.8 | 0.72 |
| L-Valine | 2.4 | 0.96 |
| L-Carnitine | 0.04 | 0.01 |
| Taurine | 0.15 | 0.06 |
| Vitamins |
Per 100 g Powder
|
Per 10 g Protein
Equivalent (1 Scoop) |
| Vitamin A, IU (mcg R.E.) (25% as beta-carotene) |
1700 (637)
|
680 (255)
|
| Vitamin D, IU (mcg) | 600 (15) | 240 (6) |
| Vitamin E, IU (mg a T.E.) | 19.1 (12.8) | 7.6 (5.1) |
| Vitamin K, mcg | 70 | 28 |
| Thiamine, mg | 1.5 | 0.6 |
| Riboflavin, mg | 1.5 | 0.6 |
| Vitamin B6, mg | 1.4 | 0.56 |
| Vitamin B12, mcg | 3 | 1.2 |
| Niacin, mg | 15.5 | 6.2 |
| Folic Acid, mcg | 300 | 120 |
| Pantothenic Acid, mg | 7.5 | 3 |
| Biotin, mcg | 30 | 12 |
| Vitamin C, mg | 60 | 24 |
| Choline, mg | 313 | 125 |
| Inositol, mg | 50 | 20 |
| Minerals |
Per 100 g Powder
|
Per 10 g Protein
Equivalent (1 Scoop) |
| Calcium, mg | 1257 | 503 |
| Phosphorus, mg | 787 | 315 |
| Magnesium, mg | 201 | 80 |
| Iron, mg | 11.3 | 4.5 |
| Zinc, mg | 10 | 4 |
| Manganese, mg | 1.9 | 0.76 |
| Copper, mg | 1 | 0.4 |
| Iodine, mcg | 115 | 46 |
| Molybdenum, mcg | 31 | 12.4 |
| Chromium, mcg | 21 | 8.6 |
| Selenium, mcg | 63 | 25 |
| Sodium, mg | 384 | 154 |
| Potassium, mg | 874 | 350 |
| Chloride, mg | 475 | 190 |
Ingredients
Sugar, Modified Corn Starch, Canola Oil, Maltodextrin, Safflower Oil, Dextrin, L-Glutamine, L-Leucine, Natural and Artificial Flavor, L-Arginine, Dicalcium Phosphate, L-Valine, L-Isoleucine, L-Asparagine Monohydrate, L-Tyrosine, Tricalcium Phosphate, L-Phenylalanine, L-Threonine, L-Proline, Potassium Citrate, L-Ornithine-Alpha Ketoglutarate, L-Alanine, Coconut Oil, Soybean Oil, L-Methionine, Sodium Citrate, Potassium Chloride, L-Glutamic Acid, L-Histidine, Choline Bitartrate, Glycine, L-Serine, L-Cystine, Flaxseed Oil, Magnesium Oxide, Ascorbyl Palmitate, Mixed Tocopherols, Rosemary Extract, Silica, L-Tryptophan, Taurine, Sodium Chloride, Ascorbic Acid, Inositol, Ferric Orthophosphate, Vitamin E Acetate, L-Carnitine, Niacinamide, Calcium Phosphate, Zinc Oxide, Sucralose (4mg/40g Powder), D-Calcium Pantothenate, Copper Gluconate, Vitamin K1, Vitamin D3, Manganese Sulfate, Vitamin A Palmitate, Mono- and Diglycerides, D-Biotin, Beta-carotene, Pyridoxine Hydrochloride, Potassium Iodide, Riboflavin, Thiamine Mononitrate, Sodium Selenite, Folic Acid, Vitamin B12, Chromium Chloride and Sodium Molybdate.
Preparation & Storage
Medical food for the dietary management of glutaric aciduria type-1 (GA-1) in children,
teens and adults, including pregnant women and woman of child-bearing age.
Administration
Use only under the direction of a physician or dietitian. GlutarAde Essential must
be consumed in conjunction with natural protein, fluid and other nutrients in quantities
prescribed by a physician or dietitian to meet total protein and general nutrient
requirements. Fat, carbohydrate and low protein sources may be used to supply needed
calories and to fulfill essential fatty acid requirements.
The recommended intake of GlutarAde Essential will vary depending on the age, body
weight and medical condition of the individual. Intake is adjusted to maintain normal
growth and development. The daily intake of GlutarAde Essential should be divided
into equal portions and distributed throughout the day.
Mixing Instructions
Add prescribed amount of GlutarAde Essential to recommended amount of cold water,
shake or stir until completely mixed together. For better accuracy, powder should
be weighed on a gram scale. Dilution may be adjusted to taste. Once prepared, store
formula in a refrigerator for no more than 24 hours from the time of preparation.
Shake or stir prepared formula immediately before use. Do not heat, bake or add
to food or beverages above 130°F. Best served chilled. Additional fluids should
be offered at the same time.
Recommended Dilution
GlutarAde Essential - Add contents of 1 scoop or pouch (40g) to approx. 7 fl oz
(210 mL) of cold water.
Precautions
Must be consumed by individuals with proven glutaric aciduria type-1 (GA-1) while
under strict medical supervision. Not intended for infants. Not intended as the
sole source of nutrition. Not for parenteral use.
Storage
Store unopened can at room temperature. Do not store at extreme temperatures. Once
opened, reseal can and store in a cool, dry place (not in refrigerator) and use
within one month of opening.
Ordering Information
|
Product Code
|
Reimbursement Code
|
HCPCS Code
|
Product Packaging
|
Calories Per Unit
|
|
|
|
|
||
| 7542 | 00847-0754-22 | B4157 or B4162 | 4 x 454 g (1 lb) | 1748 |