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GlutarAde Essential GA-1

Medical foods for the dietary management of Glutaric Aciduria Type 1 (GA-1) in children and adults, including pregnant women and woman of child-bearing age.

Price: $260.81(4 x 454 g)

 


Features

  • Lysine-free
  • Low in tryptophan to prevent deficiency
  • Contains arginine
  • Complete with vitamins and minerals developed specifically to help meet needs of children with GA-1
  • Provides 25 g of protein equivalent per 100 g of powder
  • Supplemented with flaxseed oil to provide a good source of Omega-3 fatty acids
  • Osmolalilty (mOsm/kg): 797 Based on a standard dilution of 40 g powder to 7 fl oz water (210 mL)

Indication

Glutaric acidemia type I

Nutrition

Nutrients
Per 100 g Powder
Per 10 g Protein
Equivalent (1 Scoop)
Calories 
385
154
Protein Equivalent, g 
25
10
Amino Acids, g 
30
12
Lysine, mg 
0
0
Arginine, mg 
2704
1082
Tryptophan, mg
150
60
Carbohydrate, g 
45
18
Soluble Fiber, g 
3.9
1.5
Fat, g 
13
5
Saturated Fat, g 
2.3
0.92
Monounsaturated Fat, g 
7.6
3
Polyunsaturated Fat, g 
2.9
1.1
Linoleic Acid, mg 
2232
893
a-Linolenic Acid, mg 
687
275
     
Amino Acids, g
Per 100 g Powder
Per 10 g Protein
Equivalent (1 Scoop)
L-Alanine 1.2 0.48
L-Arginine 2.7 1.08
L-Asparagine 1.8 0.72
L-Cystine 0.45 0.18
L-Glutamic Acid 0.9 0.36
L-Glutamine 4.51 1.8
Glycine 0.6 0.24
L-Histidine 0.9 0.36
L-Isoleucine 2.1 0.84
L-Leucine 3.46 1.38
L-Lysine 0 0
L-Methionine 1.02 0.41
L-Ornithine 0.6 0.24
L-Phenylalanine 1.59 0.64
L-Proline 1.5 0.6
L-Serine 0.6 0.24
L-Threonine 1.59 0.64
L-Tryptophan 0.15 0.06
L-Tyrosine 1.8 0.72
L-Valine 2.4 0.96
L-Carnitine 0.04 0.01
Taurine 0.15 0.06
     
Vitamins
Per 100 g Powder
Per 10 g Protein
Equivalent (1 Scoop)
Vitamin A, IU (mcg R.E.) (25% as beta-carotene) 
1700 (637)
680 (255)
Vitamin D, IU (mcg)  600 (15)  240 (6)
Vitamin E, IU (mg a T.E.)  19.1 (12.8)  7.6 (5.1)
Vitamin K, mcg  70 28
Thiamine, mg  1.5 0.6
Riboflavin, mg  1.5 0.6
Vitamin B6, mg 1.4 0.56
Vitamin B12, mcg  3 1.2
Niacin, mg  15.5 6.2
Folic Acid, mcg  300 120
Pantothenic Acid, mg  7.5 3
Biotin, mcg  30 12
Vitamin C, mg  60 24
Choline, mg  313 125
Inositol, mg  50 20
     
Minerals
Per 100 g Powder
Per 10 g Protein
Equivalent (1 Scoop)
Calcium, mg  1257 503
Phosphorus, mg  787 315
Magnesium, mg  201 80
Iron, mg  11.3 4.5
Zinc, mg  10 4
Manganese, mg  1.9 0.76
Copper, mg  1 0.4
Iodine, mcg  115 46
Molybdenum, mcg  31 12.4
Chromium, mcg  21 8.6
Selenium, mcg  63 25
Sodium, mg  384 154
Potassium, mg  874 350
Chloride, mg  475 190
     

Ingredients

Sugar, Modified Corn Starch, Canola Oil, Maltodextrin, Safflower Oil, Dextrin, L-Glutamine, L-Leucine, Natural and Artificial Flavor, L-Arginine, Dicalcium Phosphate, L-Valine, L-Isoleucine, L-Asparagine Monohydrate, L-Tyrosine, Tricalcium Phosphate, L-Phenylalanine, L-Threonine, L-Proline, Potassium Citrate, L-Ornithine-Alpha Ketoglutarate, L-Alanine, Coconut Oil, Soybean Oil, L-Methionine, Sodium Citrate, Potassium Chloride, L-Glutamic Acid, L-Histidine, Choline Bitartrate, Glycine, L-Serine, L-Cystine, Flaxseed Oil, Magnesium Oxide, Ascorbyl Palmitate, Mixed Tocopherols, Rosemary Extract, Silica, L-Tryptophan, Taurine, Sodium Chloride, Ascorbic Acid, Inositol, Ferric Orthophosphate, Vitamin E Acetate, L-Carnitine, Niacinamide, Calcium Phosphate, Zinc Oxide, Sucralose (4mg/40g Powder), D-Calcium Pantothenate, Copper Gluconate, Vitamin K1, Vitamin D3, Manganese Sulfate, Vitamin A Palmitate, Mono- and Diglycerides, D-Biotin, Beta-carotene, Pyridoxine Hydrochloride, Potassium Iodide, Riboflavin, Thiamine Mononitrate, Sodium Selenite, Folic Acid, Vitamin B12, Chromium Chloride and Sodium Molybdate.

Preparation & Storage

Medical food for the dietary management of glutaric aciduria type-1 (GA-1) in children, teens and adults, including pregnant women and woman of child-bearing age.

Administration
Use only under the direction of a physician or dietitian. GlutarAde Essential must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet total protein and general nutrient requirements. Fat, carbohydrate and low protein sources may be used to supply needed calories and to fulfill essential fatty acid requirements.

The recommended intake of GlutarAde Essential will vary depending on the age, body weight and medical condition of the individual. Intake is adjusted to maintain normal growth and development. The daily intake of GlutarAde Essential should be divided into equal portions and distributed throughout the day.


Mixing Instructions
Add prescribed amount of GlutarAde Essential to recommended amount of cold water, shake or stir until completely mixed together. For better accuracy, powder should be weighed on a gram scale. Dilution may be adjusted to taste. Once prepared, store formula in a refrigerator for no more than 24 hours from the time of preparation. Shake or stir prepared formula immediately before use. Do not heat, bake or add to food or beverages above 130°F. Best served chilled. Additional fluids should be offered at the same time.

Recommended Dilution
GlutarAde Essential - Add contents of 1 scoop or pouch (40g) to approx. 7 fl oz (210 mL) of cold water.

Precautions
Must be consumed by individuals with proven glutaric aciduria type-1 (GA-1) while under strict medical supervision. Not intended for infants. Not intended as the sole source of nutrition. Not for parenteral use.

Storage
Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month of opening.

Ordering Information


Product Code
Reimbursement Code
HCPCS Code
Product Packaging
Calories Per Unit

7542 00847-0754-22 B4157 or B4162 4 x 454 g (1 lb) 1748
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