MedicalFood - GlutarAde GA-1 Junior

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GlutarAde GA-1 Junior

Medical foods for the dietary management of Glutaric Aciduria Type 1 (GA-1) in children and adults, including pregnant women and woman of child-bearing age.

Features

Lysine-free
Low in tryptophan to prevent deficiency
Contains arginine
Complete with vitamins and minerals developed specifically to help meet needs of children with GA-1
Provides 10 g of protein equivalent per 100 g of powder
Supplemented with flaxseed oil to provide a good source of Omega-3 fatty acids
Osmolalilty (mOsm/kg): 426 Based on standard dilution of 20 calories per 1 fl oz water (30 mL)

Indication

Glutaric acidemia type I

Nutrition

Nutrients	Per 100 g Powder	Per 100 kcal
Calories	410	100
Protein Equivalent, g	10	2.5
Amino Acids, g	12	2.9
Lysine, mg	0	0
Arginine, mg	1080	263
Tryptophan, mg	60	14.6
Carbohydrate, g	69	17
Fat, g	10	2.5
Saturated Fat, g	2 0	0.48
Monounsaturated Fat, g	5.3	1.3
Polyunsaturated Fat, g	2.6	0.63
Linoleic Acid, mg	1901	463
a -Linolenic Acid, mg	721	176

Amino Acids, g	Per 100 g Powder	Per 100 kcal
L-Alanine	0.48	0.12
L-Arginine	1.08	0.26
L-Asparagine	0.72	0.18
L-Cystine	0.18	0.04
L-GlutamicAcid	0.36	0.09
L-Glutamine	1.8	0.44
Glycine	0.24	0.06
L-Histidine	0.36	0.09
L-Isoleucine	0.84	0.21
L-Leucine	1.38	0.34
L-Lysine	0	0
L-Methionine	0.41	0.1
L-Ornithine	0.24	0.06
L-Phenylalanine	0.64	0.16
L-Proline	0.6	0.15
L-Serine	0.24	0.06
L-Threonine	0.64	0.16
L-Tryptophan	0.06	0.01
L-Tyrosine	0.72	0.18
L-Valine	0.96	0.23
L-Carnitine	0.03	0.01
Taurine	0.06	0.01

Vitamin	Per 100 g Powder	Per 100 kcal
Vitamin A, IU (mcg R.E.)	1373 (412)	335 (101)
Vitamin D, IU (mcg)	525 (13.1)	128 (3.2)
Vitamin E, IU (mg a T.E.)	8.5 (5.7)	2.1 (1.4)
Vitamin K, mcg	34	8.3
Thiamine, mg	0.83	0.2
Riboflavin, mg	0.69	0.17
Vitamin B6, mg	0.66	0.16
Vitamin B12, mcg	1.4	0.35
Niacin, mg	6.6	1.6
Folic Acid, mcg	150	37
Pantothenic Acid, mg	6	1.5
Biotin, mcg	31	7.6
Vitamin C, mg	56	13.6
Choline, mg	213	52
Inositol, mg	125	30

Minerals	Per 100 g Powder	Per 100 kcal
Calcium, mg	460	112
Phosphorus, mg	400	97
Magnesium, mg	60	14.6
Iron, mg	8	2
Zinc, mg	7	1.6
Manganese, mg	0.43	0.1
Copper, mg	0.5	0.12
Iodine, mcg	90	22
Molybdenum, mcg	18	4.4
Chromium, mcg	12	2.9
Selenium, mcg	40	9.7
Sodium, mg	221	54
Potassium, mg	589	144
Chloride, mg	332	81

Ingredients

Corn Syrup Solids, Modified Food Starch, Canola Oil, Maltodextrin, Safflower Oil, Natural and Artificial Flavor, L-Glutamine, L-Leucine, Tricalcium Phosphate, L-Arginine, L-Valine, Coconut Oil, Soybean Oil, L-Isoleucine, L-Asparagine Monohydrate, Dipotassium Phosphate, Flaxseed Oil, L-Tyrosine, L-Phenylalanine, L-Threonine, L-Proline, Choline Bitartrate, Potassium Chloride, L-Ornithine-Alpha Ketoglutarate, L-Alanine, Magnesium Phosphate, L-Methionine, L-Glutamic Acid, L-Histidine, Glycine, L-Serine, Ascorbyl Palmitate, Sodium Citrate, Mixed Tocopherols, Rosemary Extract, L-Cystine, Sodium Chloride, Inositol, Silica, Ascorbic Acid, L-Tryptophan, Taurine, Ferrous Sulfate, Calcium Phosphate, L-Carnitine, Zinc Sulfate, Vitamin E Acetate, Niacinamide, Calcium D-Pantothenate, Mono- and Diglycerides, Vitamin A Palmitate, Vitamin D3, Copper Gluconate, Vitamin K1, D-Biotin, Manganese Sulfate, Sodium Selenite, Thiamin Mononitrate, Pyroxidine Hydrochloride, Riboflavin, Potassium Iodide, Chromium Chloride, Folic Acid, Vitamin B12 and Sodium Molybdate.

Preparation & Storage

Medical food for the dietary management of glutaric aciduria type-1 (GA-1) in young children.

Administration
Use only under the direction of a physician or dietitian. GlutarAde Junior must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet total protein and general nutrient requirements. Fat, carbohydrate and low protein sources may be used to supply needed calories and to fulfill essential fatty acid requirements.

The recommended intake of GlutarAde Junor will vary depending on the age, body weight and medical condition of the individual. Intake is adjusted to maintain normal growth and development. The daily intake of GlutarAde Junior should be divided into equal portions and distributed throughout the day.

Mixing Instructions
Add prescribed amount of GlutarAde Junior to recommended amount of cold water, shake or stir until completely mixed together. For better accuracy, powder should be weighed on a gram scale. Dilution may be adjusted to taste. Once prepared, store formula in a refrigerator for no more than 24 hours from the time of preparation. Shake or stir prepared formula immediately before use. Do not heat, bake or add to food or beverages above 130°F. Best served chilled. Additional fluids should be offered at the same time.

Dilution

Dilution of 20 Calories per 1 fluid ounce

Make Approx.	Water	Amount of Powder
2 fl oz	2 fl oz	9.8g (approx. 1 scoop)
4 fl oz	4 fl oz	19.5g (approx. 2 scoops)
6 fl oz	6 fl oz	29g (approx. 3 scoops)
8 fl oz	8 fl oz	39g (approx. 4 scoops)

The above numbers are approximate. For better accuracy, use a gram scale

Precautions

Must be consumed by individuals with proven glutaric aciduria type-1 (GA-1) while under strict medical supervision. Not intended for infants. Not intended as the sole source of nutrition. Not for parenteral use.

Storage

Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month of opening.

Ordering Information

Product Code	Reimbursement Code	HCPCS Code	Product Packaging	Calories Per Unit

7510	00847-0751-02	B4157 or B4162	4 x 400 g (14.01 oz)	1640