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UCD Anamix Junior

A powdered medical food for patients with Urea Cycle Disorder.

A powdered medical food containing essential amino acids (with increased levels of branched chain amino acids (BCAAs) and tryptophan), carbohydrates, fat, vitamins and mineral; for the dietary management of urea cycle disorders (UCD);hyperammonemia, hyperornithinemia, homocitrullinemia (HHH) syndrome; and gyrate atrophy in patients over the age of 1.

Price: $225.46(6 X 400 g (14 oz))


 


Features

  • Contains essential amino acids to help maintain a positive nitrogen balance in UCD
  • Amino acid profile rich in BCAAs for efficient and optimal protein synthesis for children with UCD
  • Sufficient non-protein calories to prevent protein being broken down for energy and toxic metabolites being produced
  • Essential micronutrients such as calcium, vitamin D, iron and zinc supplied to compensate for low intake from natural food
  • Available in unflavored and vanilla flavor
  • Osmolality (at a 1 to 3.5 dilution): 1040 mOsm/kg
  • Displacement: 0.70 mL/g

Indication

  • Urea Cycle Disorders (UCD)
  • Hyperammonemia, Hyperornithinemia, Homocitrullinemia (HHH) syndrome
  • Gyrate atrophy

Nutrition

Nutrients Per 100g Per 10g Protein
Equivalent
Calories 385 321
Protein Equivalent,g 12 10
Fat,g 17 14.2
Carbohydrate,g 46 38.3
     
Amino Acids,g Per 100g Per 10g Protein
Equivalent
L-Alanine None None
L-Arginine None None
L-Asparagine None None
L-Aspartic Acid None None
L-Citrulline None None
L-Cystine 0.43 0.36
L-Glutamic Acid None None
L-Glutamine None None
Glycine None None
L-Histidine 0.51 0.43
L-Isoleucine 2.26 1.88
L-Leucine 3.82 3.18
L-Lysine 1.92 1.6
L-Methionine 0.4 0.33
L-Phenylalanine 0.67 0.56
L-Proline None None
L-Serine None None
L-Threonine 1.59 1.33
L-Tryptophan 0.48 0.4
L-Tyrosine 1.23 1.03
L-Valine 2.29 1.91
L-Carnitine 0.009 0.008
Taurine 0.069 0.058
     
Vitamins Per 100g Per 10g Protein
Equivalent
Vitamin A, IU (mcg R.E.) 3197(960) 2664(800)
Vitamin D, IU (mcg) 920(23) 767(19.2)
Vitamin E, IU (mg a T.E.) 27.5(18.5) 22.9(15.4)
Vitamin K, mcg 92.2 76.8
Thiamine, mcg 1.9 1.6
Riboflavin, mcg 1.5 1.3
Vitamin B6, mcg 1.5 1.3
Vitamin B12, mcg 3.8 3.2
Niacin, mcg 9.6 8
Folic Acid, mcg 461 384
Pantothenic Acid, mcg 6.1 5.1
Biotin, mcg 34.6 28.8
Vitamin C, mg 120 100
Choline, mg 480 400
Inositol, mg 108 90
     
Minerals Per 100g Per 10g Protein
Equivalent
Calcium, mg 1555 1296
Phosphorus, mg 1555 1296
Magnesium, mg 246 205
Iron, mg 26.9 22.4
Zinc, mg 21.1 17.6
Manganese, mg 3.6 3
Copper, mcg 1900 1583
Iodine, mcg 276 230
Molybdenum, mcg 63.4 52.8
Chromium, mcg 41.3 34.4
Selenium, mcg 76.8 64
Sodium, mg(mmol) 1114(48.4) 928(40.3)
Potassium, mg(mmol) 1613(41.3) 1344(34.4)
Chloride, mg(mmol) 864(24.3) 720(20.3)

Ingredients

Unflavored: Unflavored: Corn Syrup Solids, Refined Vegetable Oils (High Oleic Safflower, Canola, Fractionated Coconut), Sugar, L-Leucine, Sodium Phosphate Dibasic, Tripotassium Citrate, Tricalcium Citrate, Tricalcium Phosphate, L-Lysine Hydrochloride, L-Valine, L-Isoleucine, Magnesium Hydrogen Phosphate, L-Threonine, Choline Bitartrate, L-Tyrosine, Potassium Chloride, Citric Acid Ester of Mono- And Diglycerides (An Emulsifier), L-Phenylalanine, L-Histidine, L-Tryptophan, L-Cystine, L-Methionine, L-Ascorbic Acid, M-Inositol, Ferrous Sulfate, Taurine, Zinc Sulfate, DL-alpha Tocopheryl Acetate, Manganese Sulfate, Niacinamide, L-Carnitine, Calcium-D-Pantothenate, Cupric Sulfate, Thiaminee Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Folic Acid, Potassium Iodide, Sodium Selenite, Chromium Chloride, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin.

Vanilla flavored version also contains: Artificial flavor.

Preparation & Storage

Directions for Use
Must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet protein and general nutrition requirements.

Recommended intake of UCD Anamix Junior is dependent on age, body weight and medical condition of the individual. Intake is adjusted to maintain normal growth and development. For accuracy, weigh on a gram scale. The daily intake should be divided into equal portions and distributed throughout the day.

Mixing Instructions

  • Best served chilled with meals.
  • Pour the required volume of cold water into a glass or cup.
  • Add the prescribed amount of UCD Anamix Junior powder to the water and stir. For accuracy it is recommended to use a gram scale.

It is recommended that UCD Anamix Junior be prepared at a 1 to 3.5 dilution. This dilution is a guideline only. An alternative dilution may be recommended by a clinician or dietitian (e.g. drink or paste). If given in a more concentrated form, water or diluted drinks should be offered at the same time.

Dilution Guidelines for UCD Anamix Junior
Dilution
Amount of Powder
Volume of Water
Approx. PE
1 to 3.5
50 g (10 scoops)
175 mL (approx. 6 fl oz)
6.0 g


Precautions
Must only be used under strict medical supervision.   Not intended for use as the sole source of nutrition.

Storage

  • Must only be given under strict medical supervision to patients with proven urea cycle disorders.
  • Not intended for children under one year of age. Not suitable as the sole source of nutrition. Not for parenteral use.

Ordering Information

Product Code
Reimbursement Code
HCPCS Code
Product Packaging
Calories Per Unit
 
59292 - Unflavored 49735-019292 B4157 or B4162 6 X 400 g (14 oz) 1540
 
59293 - Vanilla 49735-019293 B4157 or B4162 6 X 400 g (14 oz) 1540
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