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XLys - XTrp Maxamaid®

A lysine- and tryptophan-free powdered medical food for the dietary management of glutaric acidemia type I in children aged 1 to 8 years.

Price: $428.27(6 x 454 g (1 lb))
Please call customer service (1-800-605-0410) to request a sample or place an order.

Features

  • Lysine- and tryptophan-free
  • Contains a balanced mixture of all other essential and non-essential amino acids, carbohydrate, vitamins, minerals and trace elements
  • Age-appropriate DRI formulation
  • XLys, XTrp Maxamaid provides 25 g of protein equivalent per 100 g of powder
  • Available in orange flavor
  • Does not contain fat thereby allowing greater flexibility in modifying energy intake
Indication
  • Glutaric acidemia type I

Nutrition

Nutrients Per 100g Per 10g Protein
Equivalent
Calories 324 130
Protein Equivalent,g 25 10
Fat, g <0.1 0.04
Carbohydrate, g 56 22
     
Amino Acids,g Per 100g Per 10g Protein
Equivalent
L-Alanine 1.28 0.51
L-Arginine 2.23 0.89
L-Aspartic Acid 1.86 0.74
L-Cystine 0.83 0.33
Glycine 2 0.8
L-Histidine 1.27 0.51
L-Isoleucine 2 0.8
L-Leucine 3.42 1.37
L-Lysine None None
L-Methionine 0.53 0.21
L-Phenylalanine 1.51 0.6
L-Proline 2.42 0.97
L-Serine 1.49 0.6
L-Threonine 1.68 0.67
L-Tryptophan None None
L-Tyrosine 1.51 0.6
L-Valine 2.18 0.87
L-Carnitine 0.02 0.01
Taurine 0.14 0.06
L-Glutamine 1.5 0.6
     
Vitamins Per 100g Per 10g Protein
Equivalent
Vitamin A, IU (mcg R.E.) 1665(500) 666 (200)
Vitamin D, IU (mcg) 480(12) 192 (4.8)
Vitamin E, IU (mg a T.E.) 14.3(9.6) 5.7 (3.8)
Vitamin K, mcg 48 19
Thiamine, mcg 0.8 0.3
Riboflavin, mcg 0.8 0.3
Vitamin B6, mcg 0.8 0.3
Vitamin B12, mcg 2 0.8
Niacin, mcg 14.5 5.8
Folic Acid, mcg 240 96
Pantothenic Acid, mcg 3.2 1.3
Biotin, mcg 18 7.2
Vitamin C, mg 62.5 25
Choline, mg 250 100
Inositol, mg 56 22
     
Minerals Per 100g Per 10g Protein
Equivalent
Calcium, mg 810 324
Phosphorus, mg 810 324
Magnesium, mg 128 51
Iron, mg 14 5.6
Zinc, mg 11 4.4
Manganese, mcg 1.9 0.8
Copper, mcg 1000 400
Iodine, mcg 144 58
Molybdenum, mcg 33 13
Chromium, mcg 21.5 8.6
Selenium, mcg 40 16
Sodium, mg(mEq) 580(25.2) 232 (10)
Potassium, mg(mEq) 840(21.5) 336 (8.6)
Chloride, mg(mEq) 450(12.9) 180 (5.2)

Ingredients

Sugar, Corn Syrup Solids, L-Arginine L-Aspartate, Calcium Phosphate Dibasic, L-Leucine, Citric Acid, Tripotassium Citrate, L-Proline, L-Valine, Gylcine, L-Isoleucine, Artificial Flavors, L-Threonine, L-Glutamine, L-Phenylalanine, L-Tyrosine, L-Serine, L-Histidine, L-Alanine, Maltodextrin, Disodium Hydrogen Phosphate, L-Cystine, Sodium Chloride, Magnesium Acetate, N-Acetyl L-Methionine, Choline Bitartrate, Magnesium L-Aspartate, Taurine, L-Ascorbic Acid, Tricalcium Phosphate, M-Inositol, Ferrous Sulfate, Zinc Sulfate, L-Carnitine, DL-Alpha Tocopheryl Acetate, Manganese Sulfate, Niacinamide, Calcium D-Pantothenate, Cupric Sulfate, Thiamine Chloride Hydrochloride, Pyridoxine Hydrochloride, Riboflavin, Vitamin A Acetate, Artificial Colors (Beta-Carotene, Beet Red), Folic Acid, Potassium Iodide, Chromium Chloride, Sodium Selenite, Sodium Molybdate, Phylloquinone, D-Biotin, Vitamin D3, Cyanocobalamin.

Preparation & Storage

Maxamaid must be consumed in conjunction with natural protein, fluid and other nutrients in quantities prescribed by a physician or dietitian to meet protein and general nutrition requirements.

The recommended intake of Maxamaid will vary depending on the age, body weight and medical condition of the individual. Intake is adjusted to maintain normal growth and development. For accuracy, Maxamaid should be weighed on a gram scale. The daily intake of Maxamaid should be divided into equal portions and distributed throughout the day.

Maxamaid is best served with meals. Make a paste of the prescribed amount of powder with a small volume of chilled water. Gradually add sufficient water to make the desired volume. It is recommended that Maxamaid be prepared at a 1 to 7 dilution (e.g. 35 g (approx 1/4 cup) of powder plus 245 mL (approx. 8 fl oz) of water) and advance to a 1 to 5 dilution (e.g. 35 g (approx 1/4 cup) of powder plus 175 mL (approx. 6 fl oz) of water). These dilutions are guidelines only. Maxamaid may be given in a more concentrated form (e.g. drink or paste). If so, water or diluted drinks should be offered at the same time. For best taste, consume immediately. Larger volumes of prepared drink mix should be refrigerated and used within 24 hours of preparation.

Maxamaid Range
(Flavored & Unflavored)

Measure Weight
1 Cup 145 g
1/2 Cup  70 g
1/4 Cup 35 g
1 Tbsp 9 g


Precautions

Must only be consumed by individuals with proven glutaric acidemia type I
while under strict medical supervision. Not intended for children under one year of age. Not suitable as the sole source of nutrition. Not for parenteral use.
Storage

Store unopened can at room temperature. Do not store at extreme temperatures. Once opened, reseal can and store in a cool, dry place (not in refrigerator) and use within one month.

Ordering Information


Product Code
Reimbursement Code
HCPCS Code
Product Packaging
Calories Per Unit

117780 49735-0177-80

B4162

6 x 454 g (1 lb) 1471