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Milupa MSUD 2

An isoleucine-, leucine-, and valine-free powdered medical food for the dietary management of disorders of branched chain amino acid metabolism in individuals over 1 year of age.

Price: $314.97(2 x 500 g (17.6 oz))
Please call customer service (1-800-605-0410) to request a sample or place an order.

Features

  • Isoleucine-, leucine- and valine-free
  • Concentrated, unflavored powder
  • Enriched with vitamins, minerals and trace elements
  • Osmolality (at a 1 to 9 dilution): 700 mOsm/kg

Indications

  • Maple syrup urine disease (classic, inherited and intermittent forms)
  • Hypervalinemia (isoleucine and leucine should be added)
  • Alpha-Methylacetoacetic aciduria (leucine and valine should be added)
  • Ketotic hypoglycemia (leucine induced, idiopathic form) (isoleucine and valine should be added)
  • Hyperprolinemia type II, with hyperleucine-isoleucinemia (valine should be added)

Nutrition

Nutrients Per 100g Per 10g Protein
Equivalent
Calories 300 56
Protein Equivalent,g 54 10
Fat, g None None
Carbohydrate, g 21 3.9
     
Amino Acids,g Per 100g Per 10g Protein
Equivalent
L-Alanine 3.1 0.57
L-Arginine 2.7 0.5
L-Aspartic Acid 7.6 1.41
Cystine 1.8 0.33
L-Glutamic Acid 16 2.96
Glycine 1.8 0.33
L-Histidine 1.8 0.33
L-Isoleucine None None
L-Leucine None None
L-Lysine 5.4 1
L-Methionine 1.8 0.33
L-Phenylalanine 3.2 0.59
L-Proline 7.1 1.31
L-Serine 4 0.74
L-Threonine 3.6 0.67
L-Tryptophan 1.4 0.26
L-Tyrosine 3.9 0.72
L-Valine None None
     
Vitamins Per 100g Per 10g Protein
Equivalent
Vitamin A, IU (mcg R.E.) 5200(1562) 963(288)
Vitamin D, IU (mcg) 1310(32.8) 243(6)
Vitamin E, IU (mg a T.E.) 18(12) 3.3(2.2)
Vitamin K, mcg 167 31
Thiamine, mg 1.4 0.3
Riboflavin, mg 2 0.4
Vitamin B6, mg 1.5 0.3
Vitamin B12, mcg 3 0.6
Niacin, mg 24 4
Folic Acid, mcg 400 74
Pantothenic Acid, mg 11 2
Biotin, mcg 300 56
Vitamin C, mg 80 15
Choline, mg 260 48
Inositol, mg 300 56
     
Minerals Per 100g Per 10g Protein
Equivalent
Calcium, mg 1310 243
Phosphorus, mg 1010 187
Magnesium, mg 156 29
Iron, mg 15 2.8
Zinc, mg 7.8 1.4
Manganese, mg 0.7 0.1
Copper, mcg 2000 370
Iodine, mcg 120 22
Molybdenum, mcg 32 6
Sodium, mg 640 119
Potassium, mg 1330 246
Chloride, mg 990 183

Ingredients

L-amino acids (L-lysine-L-glutamate, L-glutamic acid, L-proline, L-aspartic acid, L-serine, L-tyrosine, L-threonine, L-phenylalanine, L-alanine, L-arginine, magnesium-L-aspartate, L-histidine, L-methionine, L-cystine, glycine, L-tryptophan), sugar, potassium phosphate, calcium phosphate, calcium carbonate, salt, choline bitartrate, m-inositol, ascorbic acid, ferrous sulfate, vanillin, niacinamide, vitamin E acetate, zinc sulfate, calcium-D-pantothenate, copper acetate, pyridoxine hydrochloride, Thiaminee hydrochloride, riboflavin, manganese sulfate, vitamin A acetate, biotin, folic acid, potassium iodide, vitamin K1, ammonium heptamolybdate, vitamin D3, vitamin B12.

Preparation & Storage

Directions for Preparation and Use
The amount of MSUD 2 needed to supplement total daily protein requirements (other than isoleucine, leucine and valine) depends on age, body weight and individual tolerance for isoleucine, leucine, and valine. The dose of MSUD 2 must be determined by a physician or dietitian and may need to be adjusted periodically.

The daily amount required should be divided into 3 to 5 single portions and can be taken mixed with calculated amounts of other food (e.g. beverages, fruit mousse). For accuracy, MSUD 2 should be weighed on a gram scale.

 Measure 

 Weight 

 1 Cup

 175 g

 ½ Cup

 85 g

 ¼ Cup

 40 g

 1 Tbsp

 10 g


Precaution
Must be used under medical supervision. For individuals over one year of age with proven disorders of branched chain amino acid metabolism. Not suitable as a sole source of nutrition. Not for parenteral use.

Storage
Store unopened cans at room temperature. Do not store at extreme temperatures. After opening, keep can tightly covered and store in a cool, dry place (not in the refrigerator) and use within four weeks.

Ordering Information


Product Code
Reimbursement Code
HCPCS Code
Product Packaging
Calories Per Unit

659351 81361-0935-10 B4155 2 x 500 g (17.6 oz) 1500