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Milupa UCD 2

A powdered medical food for the dietary management of Urea Cycle Disorders in individuals over 1 year of age.

Price: $390.88(2 x 500 g (17.6 oz))
Please call customer service (1-800-605-0410) to request a sample or place an order.


  • Essential amino acids
  • Concentrated, unflavored powder
  • Enriched with vitamins, minerals and trace elements
  • Osmolality (at a 1 to 9 dilution): 810 mOsm/kg


  • Carbamylphosphate synthetase deficiency (CPS) (citrulline or arginine supplementation required)
  • Ornithine transcarbamylase deficiency (OTC) (citrulline or arginine supplementation required)
  • Citrullinemia or argininosuccinic acid synthetase deficiency (AS) (arginine supplementation required)
  • Argininosuccinic acid lyase deficiency (AL) (arginine supplementation required)
  • Arginase deficiency


Nutrients Per 100g Per 10g Protein
Calories 290 43
Protein Equivalent,g 67 10
Fat,g None None
Carbohydrate,g 4.4 0.7
Amino Acids,g Per 100g Per 10g Protein
L-Alanine None None
L-Arginine None None
L-Aspartic Acid None None
L-Cystine None None
L-Glutamic Acid None None
Glycine None None
L-Histidine 3.6 0.54
L-Isoleucine 8.9 1.33
L-Leucine 15 2.24
L-Lysine 10.7 1.6
L-Methionine 7.1 1.06
L-Phenylalanine 14.1 2.1
L-Proline None None
L-Serine None None
L-Threonine 7.1 1.06
L-Tryptophan 2.8 0.42
L-Tyrosine None None
L-Valine 10.7 1.6
Vitamins Per 100g Per 10g Protein
Vitamin A, IU (mcg R.E.) 5200(1560) 780(233)
Vitamin D, IU (mcg) 1310(33) 200(4.9)
Vitamin E, IU (mg a T.E.) 18(12) 2.7(1.8)
Vitamin K, mcg 167 25
Thiamine, mcg 1.4 0.2
Riboflavin, mcg 2 0.3
Vitamin B6, mcg 1.5 0.2
Vitamin B12, mcg 3 0.5
Niacin, mcg 24 3.6
Folic Acid, mcg 400 60
Pantothenic Acid, mcg 11 1.6
Biotin, mcg 300 45
Vitamin C, mg 80 12
Choline, mg 260 39
Inositol, mg 300 45
Minerals Per 100g Per 10g Protein
Calcium, mg 1310 200
Phosphorus, mg 1010 151
Magnesium, mg None None
Iron, mg 15 2.2
Zinc, mg 7.8 1.2
Manganese, mg 0.7 0.1
Copper, mcg 2000 300
Iodine, mcg 120 18
Molybdenum, mcg 32 5
Sodium, mg 640 100
Potassium, mg 1330 200
Chloride, mg 990 148


L-Amino Acids (L-Lysine Acetate, L-leucine, L-phenylalanine, L-valine, L-isoleucine, L-methionine, L-threonine, L-histidine, L-tryptophan), sugar, potassium phosphate, calcium phosphate, calcium carbonate, salt, choline bitartrate, m-inositol, ascorbic acid, ferrous sulfate, vanillin, niacinamide, vitamin E acetate, zinc sulfate, calcium-D-pantothenate, copper acetate, pyridoxine hydrochloride, Thiaminee hydrochloride, riboflavin, manganese, Sulfate, vitamin A acetate, biotin, folic Acid, potassium iodide, vitamin K1, ammonium heptamolybdate, vitamin D3, vitamin B12

Preparation & Storage

Directions for Preparation and Use
The amount of UCD 2 needed to supplement total daily protein requirements depends on age, body weight and individual protein tolerance. The dose of UCD 2 must be determined by a physician or dietitian and adjusted periodically.

The daily amount required should be divided into 3 to 5 single portions and can be taken mixed with calculated amounts of other food (e.g. beverages, fruit mousse). For accuracy, UCD 2 should be weighed on a gram scale. 



 1 Cup

 145 g

 ½ Cup

 75 g

 ¼ Cup

 35 g

 1 Tbsp

  8 g

Must be used under medical supervision. For individuals over one year of age with proven Urea Cycle Disorders. Not suitable as a sole source of nutrition. Not for parenteral use.

Store unopened cans at room temperature. Do not store at extreme temperatures. After opening, keep can tightly covered and store in a cool, dry place (not in the refrigerator) and use within four weeks

Ordering Information

Product Code
Reimbursement Code
Product Packaging
Calories Per Unit
659361 81361-0936-10 B4155 2 x 500 g (17.6 oz) 1450